致死性家族性失眠症(FFI)
Patient Condition
??45????????????????????????????????????????????47?????????????FFI?PRNP D178N???Met129??????????????3???MMSE 26?????????????????>40mmHg?????????????????12???
Treatment Outcome
| before | ?????3???MMSE 26??????????????????12???PRNP D178N/Met129???? |
|---|---|
| after | ??????28?????????MMSE 18?????????????4-6?????????????????? |
| highlight | ??????+IVIG?????FFI???????130%???????????????????????? |