IPF-040

Idiopathic Pulmonary Fibrosis (IPF)

Seoul 54 years old female South Korea Total Cost: 299

Patient Condition

The patient was treated for progressive dyspnea for 2 years and had no history of smoking. HRCT showed extensive honeycomb and grid shadows in both lungs. Lung function: FVC 40% predicted, DLCO 25% predicted. 6MWD 200m, mMRC score 4. Oxygen therapy is needed. Advanced IPF was diagnosed (GAP score 6, stage III). It was assessed to meet the indications for lung transplantation.

Treatment Timeline

PhaseDetailsDate
Pre-transplant evaluation
Waiting period treatment
double lung transplant
Post-operative rehabilitation (months 1-3)
Long-term follow-up (Months 4-12)

Treatment Outcome

beforeFVC 40% predicted, DLCO 25% predicted, 6MWD 200m, mMRC score 4, oxygen therapy required, GAP score 6 (Phase III)
after12 months after lung transplantation, FVC accounted for 88% of predicted value (48% improvement), DLCO accounted for 82% of predicted value (57% improvement), 6MWD 500m (300m improvement), mMRC score 0
highlightThe double lung transplantation effect of a young female IPF patient was excellent. Her lung function returned to nearly normal 12 months after surgery, with a 6MWD of 500m, and she completely returned to normal life.