Patient Condition
The patient developed bulbar symptoms at the age of 41, and was diagnosed with ALS (bulbar onset) at the age of 42. On arrival, ALSFRS-R was 29, FVC was 66%, and swallowing function was moderately impaired. Progress is rapid (decrease of 1.4 points per month). Choose comprehensive supportive treatment.
Treatment Timeline
| Phase | Details | Date |
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| Emergency comprehensive assessment | | |
| Comprehensive management optimization | | |
| long-term management | | |
Treatment Outcome
| before | ALSFRS-R 29, monthly drop 1.4, FVC 66%, bulbar onset |
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| after | ALSFRS-R 24 points, 2-year decrease of 5 points (85% delay), FVC 58%(BiPAP), communication skills maintained |
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| highlight | Early PEG+BiPAP+ comprehensive management delayed the progress by 85% of bulb-onset ALS |
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